Rinsho Shinkeigaku (Clinical Neurology)

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  • Vol.54 No.12

Vol.54 No.12 contents

Presidential Address

My way to "Keep Pioneering": Integrated neuroscience and immunology research produces a paradigm shift for intractable neurological disease

Jun-ichi Kira, M.D., Ph.D.1)

CLINICA NEUROL, 54: 939|946, 2014

Educational Lecture Basic 09

Myasthenia gravis: Past, present and future

Hiroyuki Murai, M.D., Ph.D.1)

CLINICA NEUROL, 54: 947|949, 2014

Lecture Series 06-1

Diagnosis and care of Charcot-Marie-Tooth disease

Masanori Nakagawa, M.D.1)

CLINICA NEUROL, 54: 950|952, 2014

Lecture Series 06-2

Clinical diversity, diagnosis and treatment of hereditary amyloid neuropathy

Yoshiki Sekijima, M.D., Ph.D.1)2)

CLINICA NEUROL, 54: 953|956, 2014

Lecture Series 06-3

Clinical practice of hereditary motor neuropathy (HMN) and hereditary sensory and autonomic neuropathy (HSAN)

Hiroshi Takashima, M.D., Ph.D.1)2)

CLINICA NEUROL, 54: 957|959, 2014

Fields around Neurology 05

A magnetoencephalographic study on the disruption of the neural network

Shozo Tobimatsu, M.D., Ph.D.,1)

CLINICA NEUROL, 54: 960|962, 2014

Progress of the Year 2014

Clinical picture and diagnostic criteria

Hirohisa Watanabe, M.D.1), Mari Yoshida, M.D.2) and Gen Sobue, M.D.3)

CLINICA NEUROL, 54: 963|965, 2014

Progress of the Year 2014

Multiple system atrophy and autophagy

Koichi Wakabayashi, M.D., Ph.D.1) and Kunikazu Tanji, Ph.D.1)

CLINICA NEUROL, 54: 966|968, 2014

Progress of the Year 2014

Susceptibility gene in multiple system atrophy (MSA)

Shoji Tsuji, M.D., Ph.D.1)

CLINICA NEUROL, 54: 969|971, 2014

Progress of the Year 2014

Sema4A as a biomarker predicting responsiveness to IFN β treatment

Yuji Nakatsuji, M.D.1)

CLINICA NEUROL, 54: 972|974, 2014

Progress of the Year 2014

A novel therapeutic target in neuromyelitis optica and multiple sclerosis: high mobility group box 1 (HMGB1)

Masahiro Mori, M.D., Ph.D.1)

CLINICA NEUROL, 54: 975|977, 2014

Progress of the Year 2014

Neurofascin: A novel target for combined central and peripheral demyelination

Nobutoshi Kawamura, M.D.1)

CLINICA NEUROL, 54: 978|980, 2014

Progress of the Year 2014

The role of microglia in inflammatory demyelination lesion in the central nervous system

Ryo Yamasaki, M.D., Ph.D.1)

CLINICA NEUROL, 54: 981|983, 2014

Symposium 03

Neuromuscular disease and sleep disturbance

Mitsuru Kawai, M.D.1)

CLINICA NEUROL, 54: 984|986, 2014

Symposium 03

Sleep disturbance in Parkinson's disease

Takashi Nomura, M.D., Ph.D.1), Yuichi Inoue, M.D., Ph.D.2) and Kenji Nakashima, M.D., Ph.D.1)

CLINICA NEUROL, 54: 987|990, 2014

Symposium 03

Headache and sleep disorders

Masayuki Miyamoto, M.D., Ph.D.1),Keisuke Suzuki, M.D., Ph.D.1), Tomoyuki Miyamoto, M.D., Ph.D.2) and Koichi Hirata, M.D., Ph.D.1)

CLINICA NEUROL, 54: 991|993, 2014

Symposium 03

Sleep problems in dementia

Yasunori Oka, M.D., M.Sc., Ph.D.1)

CLINICA NEUROL, 54: 994|996, 2014

Symposium 04

Progression from episodic migraine to chronic migraine

Kiyomi Yamane, M.D.1)

CLINICA NEUROL, 54: 997|999, 2014

Symposium 04

Migraine and stroke

Yasuhisa Kitagawa, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1000|1002, 2014

Symposium 04

Migraine and epilepsy

Sadatoshi Tsuji, M.D.1)

CLINICA NEUROL, 54: 1003|1005, 2014

Symposium 04

Cortical spreading depression and pain: A missing link in the pathophysiology of migraine?

Hisanori Kowa, M.D., Ph.D.1), Hiroshi Takigawa, M.D., Ph.D.1) and Kenji Nakashima, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1006|1008, 2014

Symposium 05

Hereditary spastic paraplegia: up to date

Yoshihisa Takiyama, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1009|1011, 2014

Symposium 05

Clinical aspects of hereditary spastic paraplegias

Haruo Shimazaki, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1012|1015, 2014

Symposium 05

Molecular genetics and gene analysis of hereditary spastic paraplegia

Hiroyuki Ishiura, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1016|1017, 2014

Symposium 05

Intrathecal baclofen therapy for hereditary spastic paraplegia

Takaomi Taira, M.D., Ph.D.1) and Nobuhiko Takeda, M.D.1)

CLINICA NEUROL, 54: 1018|1020, 2014

Symposium 06

Revised Japanese guidelines for the clinical management of bacterial meningitis

Harumi Ishikawa, M.D., Ph.D.1) and Satoshi Kamei, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1021|1023, 2014

Symposium 06

Diagnostic and therapeutic strategy for acyclovir-resistant herpes encephalitis

Masayuki Saijo, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1024|1027, 2014

Symposium 06

A new approach for JC virus detection and its application for PML diagnosis

Kazuo Nakamichi, Ph.D.1), Chang-Kweng Lim, D.V.M., Ph.D.1) and Masayuki Saijo, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1028|1030, 2014

Symposium 06

Identification of NMDA receptor in normal bovine ovary and ovum

Naoko Tachibana, M.D., Ph.D.1) and Shu-ichi Ikeda, M.D., Ph.D.2)

CLINICA NEUROL, 54: 1031|1033, 2014

Symposium 08

The evaluation of autonomic nervous function by assessing baroreceptor reflex

Toshimasa Yamamoto, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1034|1037, 2014

Symposium 08

Evaluation of sudomotor function

Masato Asahina, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1038|1040, 2014

Symposium 08

Sleep and autonomic function: Sleep related breathing disorders in Parkinson's disease and related disorders

Keisuke Suzuki, M.D., Ph.D.1), Masayuki Miyamoto, M.D., Ph.D.1), Tomoyuki Miyamoto, M.D., Ph.D.2) and Koichi Hirata, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1041|1043, 2014

Symposium 08

Diagnosis of small-fiber neuropathy using various autonomic function tests.

Konen Obayashi, M.D., Ph.D.1) and Yukio Ando, M.D., Ph.D.2)

CLINICA NEUROL, 54: 1044|1046, 2014

Symposium 09

Clinicopathological features of neuropathy associated with IgG4-related disease

Ken Ohyama, M.D.1), Haruki Koike, M.D., Ph.D.1), Mie Takahashi, M.D.1), Yuichi Kawagashira, M.D., Ph.D.1), Masahiro Iijima, M.D., Ph.D.1) and Gen Sobue, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1047|1049, 2014

Symposium 09

Vasculitic neuropathy: novel classification, diagnosis and treatment

Takashi Kanda, M.D.1)

CLINICA NEUROL, 54: 1050|1052, 2014

Symposium 09

Clinical features and MRI characteristics in neuralgic amyotrophy

Kazuhiro Fukushima, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1053|1055, 2014

Symposium 09

Fisher syndrome and Bickerstaff brainstem encephalitis

Satoshi Kuwabara, M.D.1)

CLINICA NEUROL, 54: 1056|1057, 2014

Symposium 12

Cognitive impairment in multiple sclerosis

Masaaki Niino, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1058|1059, 2014

Symposium 12

Gray matter lesions and cognitive impairment in multiple sclerosis

Izumi Kawachi, M.D., Ph.D.1), Etsuji Saji, M.D., Ph.D.1) and Masatoyo Nishizawa, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1060|1062, 2014

Symposium 12

Pathogenesis of cognitive impairment in multiple sclerosis

Jin Nakahara, M.D.1)

CLINICA NEUROL, 54: 1063|1065, 2014

Symposium 12

Neuronal dysfunction in multiple sclerosis

Tetsuya Mizuno, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1066|1068, 2014

Symposium 14

The infrastructure for the clinical research of muscular dystrophies: Remudy and MDCTN

En Kimura, M.D., Ph.D.1), Harumasa Nakamura, M.D.1), Satomi Mitsuhashi, M.D., Ph.D.1), Fumi Takeuchi, M.D.1), Madoka Mori-Yoshimura, M.D., Ph.D.1), Reiko Shimizu, M.D., Ph.D.1)2), Hirofumi Komaki, M.D., Ph.D.1), Yukiko K Hayashi, M.D., Ph.D.3), Ichizo Nishino, M.D., Ph.D.1), Mitsuru Kawai, M.D.4), and Shin'ichi Takeda, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1069|1070, 2014

Symposium 14

Exon Skipping Approach to Duchenne Muscular Dystorphy

Shin'ichi Takeda, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1071|1073, 2014

Symposium 14

Nonsense readthrough therapy for Duchenne muscular dystrophy

Yasuhiro Takeshima, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1074|1076, 2014

Symposium 14

Therapeutic development in myotonic dystrophy

Masanori P. Takahashi, M.D, Ph.D.1), Masayuki Nakamori, M.D, Ph.D.1) and Hideki Mochizuki, M.D, Ph.D.1)

CLINICA NEUROL, 54: 1077|1079, 2014

Symposium 17

Fasciculation potential and ALS diagnosis

Masahiro Sonoo, M.D., Ph.D.1) and Mana Higashihara, M.D., Ph.D.2)

CLINICA NEUROL, 54: 1080|1082, 2014

Symposium 17

Fasciculation potentials in ALS-significance, and relationship with clinical features

Kota Bokuda, M.D.1) and Toshio Shimizu, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1083|1085, 2014

Symposium 17

Motor nerve hyperexcitability in ALS: its pathophysiology and treatment

Kazumoto Shibuya, M.D., Ph.D.1), Sonoko Misawa, M.D., Ph.D.1) and Satoshi Kuwabara, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1086|1088, 2014

Symposium 18

Neuropsychological thinking at everyday clinical practice

Satoru Motomura, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1089|1091, 2014

Symposium 18

Communication disorder in chronic stage stroke patients

Kazuyo Tanji, M.D.1)

CLINICA NEUROL, 54: 1092|1094, 2014

Symposium 18

Neuropsychology of dementia

Etsuro Mori, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1095|1097, 2014

Symposium 22

Clinical spectrum and treatment strategy in anti-NMDA receptor encephalitis: current status and issues

Takahiro Iizuka, M.D.1), Daisuke Ishima, M.D.1), Juntaro Kaneko, M.D.1) and Kazutoshi Nishiyama, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1098|1102, 2014

Symposium 22

Anti-NMDA Encephalitis in Psychiatry; Malignant Catatonia, Atypical Psychosis and ECT

Takashi Kanbayashi, M.D., Ph.D.1)2), Ko Tsutsui, M.D., Ph.D.1), Keiko Tanaka, M.D., Ph.D.3), Yuki Omori, M.D.1), Manabu Takaki, M.D., Ph.D.4), Mayu Omokawa, M.D.1), Akane Mori, M.D.1), Hiroaki Kusanagi, M.D., Ph.D.1), Seiji Nishino, M.D., Ph.D.5), Tetsuo Shimizu, M.D., Ph.D.1)2)

CLINICA NEUROL, 54: 1103|1106, 2014

Symposium 22

Autoimmune encephalitis-update: Roles of autoantibodies in the pathogenesis

Keiko Tanaka, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1107|1109, 2014

Symposium 30

Recent findings in dermatomyositis-specific autoantibodies

Manabu Fujimoto, M.D.1)

CLINICA NEUROL, 54: 1110|1112, 2014

Symposium 30

Pathological features of myositis with myositis -specific autoantibodies

Jun Shimizu, M.D., Ph.D.1) and Tsuneyo Mimori, M.D., Ph.D.2)

CLINICA NEUROL, 54: 1113|1114, 2014

Symposium 30

Recent progress in diagnosis and pathomechanism of inclusion body myositis

Masashi Aoki, M.D.1), Naoki Suzuki, M.D.1), Masaaki Kato, M.D.1) and Hitoshi Warita, M.D.1)

CLINICA NEUROL, 54: 1115|1118, 2014

Symposium 31

Microglia in neurodegenerative disorders and neuroinflammation

Akio Suzumura, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1119|1121, 2014

Symposium 31

Neurodegenerative disease and TREM2

Kazuya Takahashi, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1122|1124, 2014

Symposium 31

The association of Parkinson's disease pathogenesis with inflammation

Shinji Saiki, M.D. Ph.D.1)

CLINICA NEUROL, 54: 1125|1127, 2014

Symposium 31

Neuroinflammation in amyotrophic lateral sclerosis

Fumito Endo, M.D., Ph.D.1) and Koji Yamanaka, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1128|1131, 2014

Symposium 32

Spontaneous seizures in a rat models of multiple prenatal lesioning

Takashi Kamada, M.D.1), Kei-ichiro Takase, M.D., Ph.D.2) and Hiroshi Shigeto, M.D., Ph.D.3)

CLINICA NEUROL, 54: 1132|1135, 2014

Symposium 32

Histopathologic features of glia in human epileptogenic brain lesions

Akiyoshi Kakita, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1136|1138, 2014

Symposium 32

Epilepsy and functional brain networks

Taira Uehara, M.D.1), Hiroshi Shigeto, M.D., Ph.D.1) and Jun-ichi Kira, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1139|1141, 2014

Symposium 32

Recent advance in research of benign adult familial myoclonus epilepsy (BAFME): Is BAFME a progressive disorder?

Takefumi Hitomi, M.D., Ph.D.1), Ryosuke Takahashi, M.D., Ph.D.2) and Akio Ikeda, M.D., Ph.D.3)

CLINICA NEUROL, 54: 1142|1145, 2014

Symposium 32

Epilepsy in the elderly

Naoki Akamatsu, M.D., Ph.D.1), Akihiro Tanaka, M.D., Ph.D.2), Mitsuhiko Yamano, M.D., Ph.D.3) and Sadatoshi Tsuji, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1146|1147, 2014

Symposium 33

Biochemical abnormality of mutant TDP-43 protein

Koji Yamanaka, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1148|1150, 2014

Symposium 33

Calpain plays a crucial role in TDP-43 pathology

Takenari Yamashita, Ph.D.1) and Shin Kwak, M.D. Ph.D.2)

CLINICA NEUROL, 54: 1151|1154, 2014

Symposium 33

Aberration of the spliceosome in amyotrophic lateral sclerosis

Tomohiko Ishihara, M.D., Ph.D.1)2), Akiyoshi Kakita, M.D., Ph.D.3), Hitoshi Takahashi, M.D., Ph.D.4), Osamu Onodera, M.D., Ph.D.2) and Masatoyo Nishizawa, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1155|1157, 2014

Symposium 01iby non designated speakersj

Clinical and neuroimaging characteristics of patients with hereditary diffuse leukoencephalopathy with spheroids (HDLS)

Takeshi Ikeuchi, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1158|1161, 2014

Symposium 01iby non designated speakersj

MRI comparison between hereditary diffuse leukoencephalopathy with axonal spheroids (HDLS) and primary progressive multiple sclerosis (PPMS)

Ban-yu Saitoh, M.D.1)

CLINICA NEUROL, 54: 1162|1164, 2014

Symposium 01iby non designated speakersj

Neuropathology of hereditary diffuse leukoencephalopathy with axonal spheroids (HDLS)

Kiyomitsu Oyanagi, M.D.1)

CLINICA NEUROL, 54: 1165|1167, 2014

Symposium 01iby non designated speakersj

The new diagnostic methods of CADASIL as differential diagnosis of HDLS

Akihiko Ueda, M.D., Ph.D.1) and Yukio Ando, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1168|1170, 2014

Symposium 05iby non designated speakersj

Diagnosis and treatment of dementia: Overview

Katsutoshi Furukawa, M.D., Ph.D.1), Aiko Ishiki, M.D.1), Naoki Tomita, M.D., Ph.D., M.P.H.1) and Hiroyuki Arai, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1171|1173, 2014

Symposium 05iby non designated speakersj

The contribution of molecular imaging research to innovative drug development

Hitoshi Shimada, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1174|1177, 2014

Symposium 05iby non designated speakersj

Development of disease modifying drugs for dementia-focusing on anti-tau drugs-

Yoshiyuki Soeda, Ph.D.1) and Akihiko Takashima, Ph.D.1)

CLINICA NEUROL, 54: 1178|1180, 2014

Symposium 05iby non designated speakersj

The drug development for overcoming dementia in Japan

Harumasa Nakamura, M.D.1)

CLINICA NEUROL, 54: 1181|1183, 2014

Symposium 06iby non designated speakersj

Classical view of cerebrospinal production, absorption and bulk flow and its criticism

Masatsune Ishikawa, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1184|1186, 2014

Symposium 06iby non designated speakersj

Lymphatic drainage of CSF and ISF from the brain: recent concept and hypothesis

Shinya Kida, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1187|1189, 2014

Symposium 06iby non designated speakersj

A hypothesis of cerebrospinal fluid formation and absorption: from the clinical viewpoint of idiopathic normal pressure hydrocephalus

Etsuro Mori, M.D., Ph.D.1) and Shinya Yamada, M.D., Ph.D.2)

CLINICA NEUROL, 54: 1190|1192, 2014

Symposium 06iby non designated speakersj

The emerging concept of the production and absorption of cerebrospinal fluid, and recent progress in the diagnosis and treatment of iNPH

Takahiko Tokuda, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1193|1196, 2014

Super Expert Session 01

Intravenous thrombolysis for acute ischemic stroke: past, present and future

Mikito Hayakawa, M.D.1)

CLINICA NEUROL, 54: 1197|1199, 2014

Super Expert Session 01

Current and future prospects of endovascular treatment for acute ischemic stroke

Tomonori Iwata, M.D., F.A.H.A.1)

CLINICA NEUROL, 54: 1200|1202, 2014

Super Expert Session 01

Neurologist and emergency neuroendovascular revascularization
-training programs for endovascular procedures-

Keisuke Imai, M.D.1), Masashi Hamanaka, M.D.1), Takehiro Yamada, M.D.1), Hidekazu Yamazaki, M.D.1), Atsushi Yamamoto, M.D.1), Kazuma Tsuto, M.D.1), Tetsuro Takegami, M.D., Ph.D.2), Kunihiko Umezawa, M.D., Ph.D.3), Eito Ikeda, M.D., Ph.D.2) and Toshiki Mizuno, M.D., Ph.D.4)

CLINICA NEUROL, 54: 1203|1206, 2014

Super Expert Session 01

Education for stroke neurologists in neuroendovascular revascularization therapy of acute ischemic stroke

Tatsuro Takada, M.D.1)

CLINICA NEUROL, 54: 1207|1210, 2014

Super Expert Session 01

Change in number of residents who plan to specialize in cerebrovascular disease and neurointervention in the Department of Neurology of Kyushu University Hospital

Shoji Matsumoto, M.D., Ph.D.1)2)

CLINICA NEUROL, 54: 1211|1213, 2014

Super Expert Session 01

Impact of comprehensive stroke team combined with vascular neurologist, neurosurgeon and endovascular interventionist for acute stroke

Yasushi Okada, M.D., Ph.D.1), Yoshiki Sambongi, M.D.1), Yuichiro Tsurusaki, M.D.1), Tomoyuki Tsumoto, M.D., Ph.D.2), Shinji Nagata, M.D., Ph.D.3) and Masahiro Yasaka, M.D., Ph.D.1)

CLINICA NEUROL, 54: 1214|1216, 2014